Congenital Melanocytic Hairy Nevi in a Child from North-Western Nigeria

Main Article Content

Fatima Bello Jiya
Maryam Amodu- Sanni
Nma Muhammed Jiya
Dada Muhammed Aquib
Muhammed Umar
Mohammed Hassan Abba
Fa’iza Mu’azu Abubakar


Aim: To present the first report of a large congenital melanocytic nevus with satellite nevi in an apparently healthy child from Sokoto, North-Western Nigeria.

Presentation of Case: A three year old girl was brought to the paediatric out-patient clinic of Paediatrics department of Usmanu Danfodiyo University Teaching Hospital (UDUTH) Sokoto with complaints of darkened skin colour on the left side of the face and scalp, the left arm, lower back, buttocks, and thighs, and excessive hair growth over the same side of the face since birth. There were no neurological symptoms Physical examination findings revealed a well-nourished, not ill looking child. She had a hyper pigmented patch on the left side of the face extending from the lower jaw to the scalp, measuring 21 cm in its longest length, with hypertrichosis on the same site, and two distinct, firm, painless nodular lesions on the left temporal region measuring 3 mm and 4mm respectively. On the lower one-third of the left arm was a hairy, velvety area of hyperpigmentation measuring 2X3 cm in diameter. Other affected sites were the lower back, the gluteal region and the thighs. Her neurologic and other systemic examinations were normal. A diagnosis of large congenital facial melanocytic hairy nevus with multiple satellite nevi was made.

Discussion: Congenital melanocytic nevi are benign proliferations of melanocytic cells said to be present at birth or in the first two years of life. Large lesions are rare, they measure 20 cm or more and are said to occur more commonly on the trunk and thighs. The exact pathogenesis of congenital melanocytic nevi is yet, unknown. It is thought to occur as a result of a morphological error in the neuroectoderm during embryogenesis. Treatment of patients with large congenital melanocytic nevus may include surgical or non-surgical procedures as well as psychological interventions. Large lesions, multiple satellite lesions or paravertebral and axial locations are sometimes associated with the risk of neurological complications and malignant transformation.

Conclusion: Large congenital melanocytic nevi are uncommon skin lesions that can occur in apparently healthy children. Individualization of the patients with regards to treatment options and long term monitoring are imperative.

Congenital, large, melanocytic nevi, child, Sokoto, Nigeria

Article Details

How to Cite
Jiya, F. B., Sanni, M. A.-, Jiya, N. M., Aquib, D. M., Umar, M., Abba, M. H., & Abubakar, F. M. (2020). Congenital Melanocytic Hairy Nevi in a Child from North-Western Nigeria. Asian Journal of Medicine and Health, 18(7), 28-34.
Case Study


Grichnik JM, Rhodes AR, Sober AJ. Benign neoplasias and hyperplasias of melanocytes. In: Wolff K, Goldsmith LA, Katz SI, Gilchrest BA, Paller AS, Lefell DJ, editors. Fitzpatrick's Dermatology in General Medicine. 7th Ed. New York: McGraw-Hill. 2008;1099–1122.

Kincannon J, Boutzale C. The physiology of pigmented nevi. Pediatrics. 1999;104: 1042–1045.

Arneja J, Gosain A. Giant congenital melanocytic nevi. Plast Reconstr Surg. 2007;120:26–40.

Castilla EE, da Graça Dutra M, Orioli-Parreiras IM. Epidemiology of congenital pigmented naevi: I. Incidence rates and relative frequencies. Br. J. Dermatol. 1981; 104:307–315.

Slutsky JB, Barr JM, Femia AN, Marghoob AA. Large congenital melanocytic nevi: associated risks and management considerations. Semin Cutan Med Surg. 2010;29:79–84.

Viana ACL, Gontijo B, Bittencourt FV. Giant Congenital melanocytic nevus. An Bras Dermatol. 2013;88:863-878.

Koot HM, de Waard-van der Spek F, Peer CD, Mulder PG, Oranje AP. Psychosocial sequelae in 29 children with giant congenital melanocytic naevi. Clin Exp. Dermatol. 2000;25:589–593

Saida T. Histogenesis of congenital and acquired melanocytic nevi: A unifying concept. Am J Dermatopathol. 2006;28: 377–379.

Tromberg J, Bauer B, Benvenuto-Andrade C, Marghoob AA. Congenital melanocytic nevi needing treatment. Dermatol Ther. 2005;18:136–150.

Marghoob AA. Congenital melanocytic nevi. Evaluation and management. Dermatol Clin. 2002;20:607-16.

DeDavid M, Orlow SJ, Provost N, Marghoob AA, Rao BK, Wasti Q, et al. Neurocutaneous melanosis: Clinical features of large congenital melanocytic nevi in patients with manifest central nervous system melanosis. J Am Acad Dermatol. 1996;35:529-38.

Krengel S, Hauschild A, Schäfer T. Melanoma risk in congenital melanocytic naevi: A systematic review. Br J Dermatol. 2006;155:1–8.

From L. Congenital nevi--let's be practical. Pediatr Dermatol. 1992;9:345–346.

Kinsler V, Bulstrode N. The role of surgery in the management of congenital melanocytic naevi in children: A perspective from Great Ormond Street Hospital. J Plast Reconstr Aesthet Surg. 2009;62:595–601.